Adult Cystic Fibrosis

Authors: Frank Edenborough, Shammi L Ramlakhan / Editor: Jason M Kendall / Reviewer: Kaja Mohammad Rasheed / Codes: A2 / Published: 15/10/2019

Describing the pathophysiology of cystic fibrosis.

After completing this session you will be able to:

  • Describe the pathophysiology of cystic fibrosis
  • Appreciate that patients with cystic fibrosis are surviving longer
  • Describe the chronic complications of cystic fibrosis and identify those conditions most likely to result in presentation to the ED
  • Recognise unique problems with cystic fibrosis that may present to the emergency department
  • Identify scenarios where emergency department treatment differs between cystic fibrosis patients and non-cystic fibrosis patients


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Please use the following resources for more information:

  • European CF Diagnostic Working Group view link. (Last accessed September 2019).
  • Guidelines for Diagnosis of Cystic Fibrosis in Newborns through Older Adults: Cystic Fibrosis Foundation Consensus Report Farrell, Philip M. et al. The Journal of Pediatrics, Volume 153, Issue 2, S4 – S14. (Last accessed September 2019).

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